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Resumen de Eritrozitosiaren maneiua pediatrian

Libe Lizarraga Navarro

  • euskara

    Eritrozitosia pediatrian oso ezohikoa da eta intzidentzia zehatza zein den jakitea zaila da. Umeetan zein helduetan kausarik ohikoena hipoxemiaren ondoriozko eritropoietinaren handitze fisiologikoak eragindakoa da. Pediatrian, eritrozitosiaren bigarren kausa ohikoena sortzetikoa da; helduetan, aldiz, hartutakoa; zehazki, polizitemia vera.

    Helduetarako, eritrozitosiaren maneiurako algoritmoak daude, polizitemia vera baztertzea helburu dutenak. Pediatrian, ordea, ez dago berariazko algoritmorik. Hori dela eta, ikerketa honek helduetan erabiltzen den algoritmo-diagnostikoak pediatrian duen baliogarritasuna eta pediatriarako algoritmo egokiagoak aztertzea du helburu.  Berrikuspen bibliografikoa egin ostean, pediatrian eritrozitosiaren maneiurako berariazko algoritmoa izatea baliagarria dela ondorioztatu dugu. Algoritmoa helduekiko ezberdina izan behar da, bi populazioen artean dauden ezberdintasun etiologikoak direla eta. Pediatriarako proposatzen den algoritmoan, lehenik eta behin, eritrozitosia eragin dezaketen kausa sekundarioak aztertu behar dira. Behin eritrozitosia baieztatu eta kausa sekundarioak baztertuta, sortzetiko kausak bilatu beharko dira. Horretarako, pazientea erreferentziazko onkohematologia pediatrikoko zerbitzura bideratuko da, ikerketa sakontzeko helburuarekin.

  • English

    Erythrocytosis in pediatrics is very rare, making it difficult to estimate an exact incidence. In both adults and children, the most common cause is due to a physiological increase in EPO. The second most common cause in pediatrics would be congenital, however in adults it would be acquired, specifically, Polycythemia Vera.

    In adults there is an algorithm for the management of erythrocytosis, which is focused on ruling out Polycythemia Vera. However, in pediatrics there are no algorithms. For this reason, we have proposed this research, on the one hand, to assess whether the algorithm used in adults can be extrapolated, and second, to define what the algorithm should be in children.

    With this bibliographic review we have concluded that an algorithm for the management of erythrocytosis in pediatrics is useful but must be different from that of adults, because the etiology in both groups is different. Initially, in children, erythrocytosis secondary to another cause must be ruled out, and once all possibilities have been ruled out, congenital causes must be sought. To do this, the patient will be referred to the Oncohematology referral service, with the aim of expanding the study.


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