Síndrome de Poems: Caso clínico

• Pabla Horta H ^[1] ; Iván Quevedo L ^[1]
  1. [1] Universidad de Concepción

     Universidad de Concepción

     Comuna de Concepción, Chile

     
• Localización: Revista Médica de Chile, ISSN-e 0034-9887, Vol. 132, Nº. 4, 2004, págs. 481-484
• Idioma: español
• Títulos paralelos:
  • Poems syndrome: Report of one case
• Enlaces
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• Resumen

  • Poems syndrome (polyneuropathy, organomegaly, endocrine abnormality, M-protein, plasma cell dyscrasia, and skin lesions) is a plasma cell dyscrasia whose pathogenesis is unknown. We report a 60 years old woman that presented a tetraparesis caused by a sensitive motor polyneuropathy. The subsequent work up revealed an IgA type monoclonal gammopathy, hepatomegaly, hyperestrogenism, primary adrenal failure, hypothyroidism, hyperpigmentation and erythematous lesions in the skin and ankle edema. The patient is being treated with prednisone 0.5 mg/kg and levothyroxine 100 µg/day, with partial remission of her symptoms (Rev Méd Chile 2004; 132: 485-8)