Hemangioendotelioma epitelioide pulmonar: Reporte de un caso

• Manuel Quiroz ^[2] ; Álvaro Undurraga ^[3] ; Rafael Moya ^[1] ; Cristina Fernández ^[1] ; Katiuska Bezares ^[1] ; Virginia Linacre ^[4]
  1. [1] Hospital del Salvador

     Hospital del Salvador

     Santiago, Chile

     
  2. [2] Hospital Clínico San Borja Arriarán
  3. [3] Instituto Nacional del Tórax Servicio Medicina Broncopulmonar
  4. [4] Instituto Nacional del Tórax Servicio Cirugía Torácica

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• Localización: Revista Médica de Chile, ISSN-e 0034-9887, Vol. 145, Nº. 5, 2017, págs. 662-666
• Idioma: español
• Títulos paralelos:
  • Lung epithelioid hemangioendothelioma: Report of one case
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• Resumen

  • Epithelioid hemangioendothelioma is a multifocal tumor that rarely metastasizes. It is difficult to diagnose, most often it is an incidental finding in young asymptomatic women. The radiologic pattern is heterogeneous. Histologic confirmation of Weibel-Palade bodies or immunohistochemistry based on specific tumor markers such as factor VIII and CD34 are the most important finding to confirm the diagnosis. We report a 21 years old woman Presenting with cough and dyspnea. A chest X ray was suggestive of tuberculosis. Sputum smears were negative for acid fat bacilli and the tuberculin test was negative. A chest CAT scan showed multiple nodular lesions. A surgical biopsy of the lesions confirmed the presence of a hemangioendothelioma. The patient was initially treated with prednisone and azathioprine without response. Thereafter, the patient is without treatment and without evidence of disease progression.