Resumen de Osteogenesis imperfecta: oral and medical disorders in children

Jorge Carballido Fernández, Marta Monteserín Matesanz, Mª Rosa Mourelle Martínez, Joaquín de Nova García

• Introduction: Osteogenesis imperfecta, also called the brittle bone disease, is a condition characterised by a disorder in the connective tissues of the entire body, including the teeth. The objective of the study was to evaluate the presence of fractures and the bones affected, the presence of dentinogenesis imperfecta, the treatment of osteogenesis imperfecta and the type of bisphosphonate administered.

  Method: The clinical histories of 17 patients with osteogenesis imperfecta were evaluated.

  Results: Of the patients, 81% suffered fractures, 24% in the femur, 53% of the patients presented dentinogenesis imperfecta, 71% of the patients are treated with bisphosphonates and 83% with pamidronate.

  Conclusions: The majority of the patients have suffered fractures during their lives, dentinogenesis imperfecta is frequent in these patients and the majority of them are under treatment with bisphosphonates.