Cutaneous mastocytosis in the adult: what lies beneath

• LilianaTorres ^[1] ; Francisco Bento Soares ^[1] ; Diana Pereira Anjos ^[1] ; Mari Mesquita ^[1]
  1. [1] Centro Hospitalar do Tâmega e Sousa

     Centro Hospitalar do Tâmega e Sousa

     Penafiel, Portugal

     
• Localización: Galicia Clínica, ISSN 0304-4866, ISSN-e 1989-3922, Vol. 81, Nº. 1 (Enero), 2020, págs. 19-20
• Idioma: inglés
• Enlaces
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• Resumen

  • Mastocytosis is a disorder characterized by clonal mast cell proliferation and accumulation within various organs, most commonly, the skin. Adult-onset mastocytosis is highly suggestive of a systemic involvement and the cases limited to the skin are uncommon. The authors report a 61-year-old male with pruritus associated with hyperpigmented maculopapular skin lesions and a positive Darier’s sign. The skin biopsy revealed spindle mast cells infiltrations. The bone marrow study was normal. He started on H1 antihistamines with significant clinical improvement