Unique cardiac anomaly due to lateralization of a straight trunco-conal septum

• Autores: Asit Kumar Sikary, Shivani Dhaka, Tony George Jacob
• Localización: European Journal of anatomy, ISSN-e 1136-4890, Vol. 21, Nº. 2, 2017, págs. 157-160
• Idioma: inglés
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• Resumen

  • Congenital heart disease is present in 4-50/1000 live births worldwide, causing about 10% of infant mortality. Congenital heart disease arises when there is a defect in the process of development of the heart through looping, remodeling, realignment and septation of the primitive endothelial tube. Here we describe a case of congenital heart disease where there was formation of straight truncoconal septum with lateralization. It has caused transposition of great vessels, atretic non communicating stenosed pulmonary trunk, and blind outflow tract of left ventricle. There was renal anomaly too in the form of horseshoe kidney. The entire developmental anomaly could be traced back to the period between the 6th and the 9th week of intrauterine life. The neonate died within half an hour of birth.