Distrofia simpático-refleja y mioclonías: una asociación infrecuente

• Autores: M. Álvarez Fuente, Esther Aleo Luján, E. Cascón Criado, G. Galindo Doncel, V. San Antonio Arce
• Localización: Anales de Pediatría: Publicación Oficial de la Asociación Española de Pediatría ( AEP ), ISSN-e 1696-4608, ISSN 1695-4033, Vol. 76, Nº. 1, 2012, págs. 38-40
• Idioma: español
• Títulos paralelos:
  • Complex regional pain syndrome and myoclonus: an uncommon combination
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• Resumen

  • Abstract Complex regional pain syndrome (CRPS) is quite uncommon in paediatric patients. There is no identified organic aetiology. CRPS has a very significant psychosomatic component; therefore it is necessary to take a multidisciplinary approach to its treatment, which should include psychiatric assessment. CRPS is very difficult to diagnose, and can take months to control its symptoms. The association with myoclonus is rare, and since myoclonus is the clinical manifestation of a vast spectrum of different neurological disorders, some of which are degenerative, it is important to make a diagnosis as quickly as possible.

    We present the case of an adolescent male with an atypical presentation of CRPS. CRPS was located in the thorax, which is very unusual and was associated with myoclonus and dystonias. This made the diagnosis harder and widened the aetiological spectrum.