Pheochromocytomas and Paragangliomas

• Alkaissi, Hussam ^[1] ; Taieb, David ^[3] ; K. Ghayee, Hans ^[2]
  1. [1] National Institute of Diabetes and Digestive and Kidney Diseases

     National Institute of Diabetes and Digestive and Kidney Diseases

     Estados Unidos

     
  2. [2] University of Florida

     University of Florida

     Estados Unidos

     
  3. [3] Department of Nuclear Medicine, Aix-Marseille University, La Timone University Hospital, Marseille, France

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• Localización: Endocrinology and metabolism clinics of North America, ISSN 0889-8529, Vol. 55, Nº. 2, 2026, págs. 317-344
• Idioma: inglés
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  • PPGL are rare neuroendocrine tumors that secrete catecholamines. There are over 20 driver mutations associated with PPGL. It is recommended that patients who are diagnosed with PPGL get genetic testing. Biochemical diagnosis is made by showing significant elevations in plasma and/or urine MN. Localizations studies include CT, MRI, and functional imaging such as PET scans. Alpha-blockers are a central component for preparation prior to surgical removal of the tumor which is the mainstay for